Extracorporeal membrane oxygenation support for balloon atrial septostomy in a BMPR2 variant‐associated pulmonary arterial hypertension

医学 体外膜肺氧合 心脏病学 肺动脉高压 内科学 气球 BMPR2型 充氧 生物化学 化学 基因 骨形态发生蛋白
作者
Shouji Fukuoka,Noriyuki Kaku,Hazumu Nagata,Yusaku Nagatomo,Kanako Higashi,Daisuke Toyomura,Yoshihiro Hirata,Keiichi Hirono,Kenichiro Yamamura,Shouichi Ohga
出处
期刊:Pediatric Pulmonology [Wiley]
标识
DOI:10.1002/ppul.26973
摘要

Pediatric PulmonologyEarly View CLINICAL CORRESPONDENCE Extracorporeal membrane oxygenation support for balloon atrial septostomy in a BMPR2 variant-associated pulmonary arterial hypertension Shoji Fukuoka MD, Shoji Fukuoka MD orcid.org/0000-0002-1296-4507 Emergency and Critical Care Center, Kyushu University, Fukuoka, Japan Department of Pediatrics, Graduate School of Medical Sciences, Kyushu University, Fukuoka, Japan Contribution: Writing - original draft, Conceptualization, Data curationSearch for more papers by this authorNoriyuki Kaku MD, PhD, Corresponding Author Noriyuki Kaku MD, PhD [email protected] orcid.org/0000-0001-6803-4635 Emergency and Critical Care Center, Kyushu University, Fukuoka, Japan Department of Pediatrics, Graduate School of Medical Sciences, Kyushu University, Fukuoka, Japan Correspondence Noriyuki Kaku, MD, PhD, Department of Pediatrics, Graduate School of Medical Sciences, Kyushu University, 3-1-1 Maidashi, Higashi- ku, Fukuoka 812-8582, Japan. Email: [email protected] Contribution: Conceptualization, Data curation, Writing - original draftSearch for more papers by this authorHazumu Nagata MD, PhD, Hazumu Nagata MD, PhD Department of Pediatrics, Graduate School of Medical Sciences, Kyushu University, Fukuoka, Japan Contribution: Writing - original draft, Data curationSearch for more papers by this authorYusaku Nagatomo MD, PhD, Yusaku Nagatomo MD, PhD Department of Pediatrics, Graduate School of Medical Sciences, Kyushu University, Fukuoka, Japan Contribution: Data curation, Formal analysis, Writing - original draftSearch for more papers by this authorKanako Higashi MD, Kanako Higashi MD Emergency and Critical Care Center, Kyushu University, Fukuoka, Japan Department of Pediatrics, Graduate School of Medical Sciences, Kyushu University, Fukuoka, Japan Contribution: Data curation, Writing - review & editingSearch for more papers by this authorDaisuke Toyomura MD, Daisuke Toyomura MD Emergency and Critical Care Center, Kyushu University, Fukuoka, Japan Contribution: Data curation, Writing - review & editingSearch for more papers by this authorYuichiro Hirata MD, Yuichiro Hirata MD Department of Pediatrics, Graduate School of Medical Sciences, Kyushu University, Fukuoka, Japan Contribution: Data curation, Writing - review & editingSearch for more papers by this authorKeiichi Hirono MD, PhD, Keiichi Hirono MD, PhD Department of Pediatrics, Faculty of Medicine, University of Toyama, Toyama, Japan Contribution: Writing - review & editing, ​InvestigationSearch for more papers by this authorKenichiro Yamamura MD, PhD, MSc, Kenichiro Yamamura MD, PhD, MSc orcid.org/0000-0002-5684-1330 Department of Pediatrics, Graduate School of Medical Sciences, Kyushu University, Fukuoka, Japan Contribution: Data curation, Supervision, Writing - review & editingSearch for more papers by this authorShouichi Ohga MD, PhD, Shouichi Ohga MD, PhD Department of Pediatrics, Graduate School of Medical Sciences, Kyushu University, Fukuoka, Japan Contribution: Conceptualization, Writing - original draft, Writing - review & editingSearch for more papers by this author Shoji Fukuoka MD, Shoji Fukuoka MD orcid.org/0000-0002-1296-4507 Emergency and Critical Care Center, Kyushu University, Fukuoka, Japan Department of Pediatrics, Graduate School of Medical Sciences, Kyushu University, Fukuoka, Japan Contribution: Writing - original draft, Conceptualization, Data curationSearch for more papers by this authorNoriyuki Kaku MD, PhD, Corresponding Author Noriyuki Kaku MD, PhD [email protected] orcid.org/0000-0001-6803-4635 Emergency and Critical Care Center, Kyushu University, Fukuoka, Japan Department of Pediatrics, Graduate School of Medical Sciences, Kyushu University, Fukuoka, Japan Correspondence Noriyuki Kaku, MD, PhD, Department of Pediatrics, Graduate School of Medical Sciences, Kyushu University, 3-1-1 Maidashi, Higashi- ku, Fukuoka 812-8582, Japan. Email: [email protected] Contribution: Conceptualization, Data curation, Writing - original draftSearch for more papers by this authorHazumu Nagata MD, PhD, Hazumu Nagata MD, PhD Department of Pediatrics, Graduate School of Medical Sciences, Kyushu University, Fukuoka, Japan Contribution: Writing - original draft, Data curationSearch for more papers by this authorYusaku Nagatomo MD, PhD, Yusaku Nagatomo MD, PhD Department of Pediatrics, Graduate School of Medical Sciences, Kyushu University, Fukuoka, Japan Contribution: Data curation, Formal analysis, Writing - original draftSearch for more papers by this authorKanako Higashi MD, Kanako Higashi MD Emergency and Critical Care Center, Kyushu University, Fukuoka, Japan Department of Pediatrics, Graduate School of Medical Sciences, Kyushu University, Fukuoka, Japan Contribution: Data curation, Writing - review & editingSearch for more papers by this authorDaisuke Toyomura MD, Daisuke Toyomura MD Emergency and Critical Care Center, Kyushu University, Fukuoka, Japan Contribution: Data curation, Writing - review & editingSearch for more papers by this authorYuichiro Hirata MD, Yuichiro Hirata MD Department of Pediatrics, Graduate School of Medical Sciences, Kyushu University, Fukuoka, Japan Contribution: Data curation, Writing - review & editingSearch for more papers by this authorKeiichi Hirono MD, PhD, Keiichi Hirono MD, PhD Department of Pediatrics, Faculty of Medicine, University of Toyama, Toyama, Japan Contribution: Writing - review & editing, ​InvestigationSearch for more papers by this authorKenichiro Yamamura MD, PhD, MSc, Kenichiro Yamamura MD, PhD, MSc orcid.org/0000-0002-5684-1330 Department of Pediatrics, Graduate School of Medical Sciences, Kyushu University, Fukuoka, Japan Contribution: Data curation, Supervision, Writing - review & editingSearch for more papers by this authorShouichi Ohga MD, PhD, Shouichi Ohga MD, PhD Department of Pediatrics, Graduate School of Medical Sciences, Kyushu University, Fukuoka, Japan Contribution: Conceptualization, Writing - original draft, Writing - review & editingSearch for more papers by this author First published: 19 March 2024 https://doi.org/10.1002/ppul.26973Read the full textAboutPDF ToolsRequest permissionExport citationAdd to favoritesTrack citation ShareShare Give accessShare full text accessShare full-text accessPlease review our Terms and Conditions of Use and check box below to share full-text version of article.I have read and accept the Wiley Online Library Terms and Conditions of UseShareable LinkUse the link below to share a full-text version of this article with your friends and colleagues. Learn more.Copy URL Share a linkShare onEmailFacebookTwitterLinkedInRedditWechat No abstract is available for this article. Supporting Information Filename Description ppul26973-sup-0001-S_Table_1_Final.docx24.3 KB Supporting information. Please note: The publisher is not responsible for the content or functionality of any supporting information supplied by the authors. Any queries (other than missing content) should be directed to the corresponding author for the article. REFERENCES 1Hansmann G. Pulmonary hypertension in infants, children, and young adults. J Am Coll Cardiol. 2017; 69(20): 2551-2569. 10.1016/j.jacc.2017.03.575 PubMedWeb of Science®Google Scholar 2Evans JDW, Girerd B, Montani D, et al. BMPR2 mutations and survival in pulmonary arterial hypertension: an individual participant data meta-analysis. Lancet Respir Med. 2016; 4(2): 129-137. 10.1016/S2213-2600(15)00544-5 CASPubMedWeb of Science®Google Scholar 3Puigdevall P, Piccari L, Blanco I, et al. Genetic linkage analysis of a large family identifies FIGN as a candidate modulator of reduced penetrance in heritable pulmonary arterial hypertension. J Med Genet. 2019; 56(7): 481-490. 10.1136/jmedgenet-2018-105669 CASPubMedWeb of Science®Google Scholar 4Chaikuad A, Thangaratnarajah C, von Delft F, Bullock AN. Structural consequences of BMPR2 kinase domain mutations causing pulmonary arterial hypertension. Sci Rep. 2019; 9(1):18351. 10.1038/s41598-019-54830-7 CASPubMedWeb of Science®Google Scholar 5Kumar R, Aktay-Cetin Ö, Craddock V, et al. Potential long-term effects of SARS-CoV-2 infection on the pulmonary vasculature: multilayered cross-talks in the setting of coinfections and comorbidities. PLoS Pathog. 2023; 19(1):e1011063. 10.1371/journal.ppat.1011063 CASPubMedWeb of Science®Google Scholar 6Tian W, Jiang X, Sung YK, et al. Phenotypically silent bone morphogenetic protein receptor 2 mutations predispose rats to inflammation-induced pulmonary arterial hypertension by enhancing the risk for neointimal transformation. Circulation. 2019; 140(17): 1409-1425. 10.1161/CIRCULATIONAHA.119.040629 CASPubMedWeb of Science®Google Scholar 7Lai LYS, Gracie NP, Gowripalan A, Howell LM, Newsome TP. SMAD proteins: mediators of diverse outcomes during infection. EJCB. 2022; 101(2):151204. CASWeb of Science®Google Scholar 8Sakurai K, Singhal N. Extracorporeal membrane oxygenation in children: a brief review. J Paediatr Child Health. 2022; 58(9): 1525-1531. 10.1111/jpc.16151 PubMedWeb of Science®Google Scholar 9Delmas C, Vallee L, Bouisset F, et al. Use of percutaneous atrioseptotosmy for left heart decompression during veno-arterial extracorporeal membrane oxygenation support: an observational study. J Am Heart Assoc. 2022; 11(17):e024642. 10.1161/JAHA.121.024642 PubMedWeb of Science®Google Scholar Early ViewOnline Version of Record before inclusion in an issue ReferencesRelatedInformation

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