Recent advances in the diagnosis and treatment of Kasabach-Merritt phenomenon

Kasabach - Merritt phenomenon(KMP), also known as Kasabach - Merritt syndrome, is a rare syndrome associated with Kaposiform haemangioendothelioma or tufted angioma, and characterized by thrombocytopenia and consumptive coagulopathy.KMP onsets early and progresses quickly.If diagnosis and treatment delayed, it can be life-threatening.In this paper, the progress of clinical manifestations, pathogenesis, diagnosis and treatment of KMP are summarized. Key words: Kasabach-Merritt phenomenon; Kaposiform hemangioendothelioma; Tufted angioma; Child