Association Between Leg Muscle Thickness and Walking Test with the Haemophilia-Specific Functional Parameters

医学 血友病 脚踝 生活质量(医疗保健) 关节病 物理医学与康复 物理疗法 膝关节 超声波 腓肠肌 骨骼肌 内科学 骨关节炎 外科 病理 放射科 护理部 替代医学
作者
Jia‐Pei Hong,Jiunn‐Horng Kang,Chian‐Her Lee,Chih‐Hong Lee,Shu‐Huey Chen,Yen‐Lin Liu,Jia-Ruey Tsai,Chen-Hua Tsai,Wan‐Ling Ho,Mei-Mei Cheng,Prangthip Charoenpong,Chia-Yau Chang
出处
期刊:American Journal of Physical Medicine & Rehabilitation [Ovid Technologies (Wolters Kluwer)]
标识
DOI:10.1097/phm.0000000000002482
摘要

Abstract Objective To evaluate the muscle thickness and walking test in people with haemophilia A (PWH) and their correlation to joint health and functional impairments. Design Cross-sectional study Results 29 severe/moderate PWH were enrolled. Muscle thickness of quadriceps and medial gastrocnemius were measured using ultrasound. Joint health and functional capacity were assessed using Haemophilia Joint Health Score (HJHS), Haemophilia Early Arthropathy Detection with Ultrasound (HEAD-US), 6-Minute Walking test (6MWT), Haemophilia Quality of Life Questionnaire for Adults (Haem-A-QoL), and Haemophilia Activities List (HAL). Quadriceps muscle thickness significantly correlated with HJHS knee, HEAD-US knee, and HAL. Calf muscle thickness significantly correlated with the HJHS ankle. After adjusted age and BMI, calf muscle thickness was inversely associated with the HJHS ankle. 6MWT was found to significantly correlate with HJHS total, HEAD-US total, Haem-A-QoL, and HAL. Conclusion Muscle thickness and the distance of 6MWT were linked to assessment of joint health, quality of life and activity participation in PWH. Ultrasound measurement of muscle thickness and walking test appear to be useful tools for the assessment of joint health and functional status in PWH.

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