Compliance and Complications in Catecholaminergic Polymorphic Ventricular Tachycardia

Based on this robust study, one can conclude that symptomatic pediatric CPVT patients are at high risk for arrhythmic syncope, SCA and SCD even when receiving medical treatment. Compliance and underdosing with medications play a major role in these risks. LCSD may be underutilized in CPVT. ICDs are protective against these risks but at the cost of a high rate of appropriate and inappropriate shocks and other complications.