医学
皮肤病科
阿达木单抗
化脓性汗腺炎
强直性脊柱炎
免疫学
疾病
肿瘤坏死因子α
内科学
作者
Gizem Kırmızıer,Elif Altunel Kılınç,Nurdan Oruçoğlu,Ümit Türsen
标识
DOI:10.1111/1756-185x.15114
摘要
Abstract PASS syndrome is a rare autoinflammatory disease characterized by acne vulgaris, hidradenitis suppurativa, pyoderma gangrenosum, and ankylosing spondylitis. Unlike other autoinflammatory disorders such as PAPA and PASH syndrome, there is no documented gene mutation link. Although there are no established treatment guidelines due to the rarity of these diseases, systemic corticosteroids, biologics, and immunosuppressive drugs are used currently. In our report, we presented a case of PASS syndrome who was unresponsive to adalimumab and in whom we observed improvement in both skin and joint manifestations with intravenous immunoglobulin (IVIG) and anti‐IL‐1 treatment.
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