贝里穆马布
美罗华
医学
获得性大疱性表皮松解症
大疱性表皮松解症
皮肤病科
红斑狼疮
免疫学
自身抗体
抗体
B细胞激活因子
B细胞
作者
Thomas J Tull,Emma Benton,Kristina Semkova,Natalie A. Watson,John Mee,Berta Magallares López,Jane Setterfield,Barbara Carey,Sajjad Ajmad,Scott Robbie,Richard Groves,Giovanni Sanna,David D’Cruz
摘要
We report two cases of recalcitrant epidermolysis bullosa aquisita with associated systemic lupus erythematosus treated with combination rituximab and belimumab therapy. This resulted in complete resolution of cutaneous lesions and partial response of mucosal lesions. These cases support the use of combined rituximab and belimumab for the treatment of recalcitrant immunobullous disease.
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