医学
戈登哈综合征
轨道(动力学)
桥小脑角
中颅窝
病变
磁共振成像
解剖
肿块/病变
皮样囊肿
放射科
外科
工程类
航空航天工程
作者
Mingyu Ren,Ruimiao Li,Limin Liu
出处
期刊:Ophthalmology
[Elsevier]
日期:2022-10-27
卷期号:130 (9): 913-913
标识
DOI:10.1016/j.ophtha.2022.09.019
摘要
A 2-year-old boy presented with a mass protruding from his left eye. He had epibulbar dermoids on that eye and skin lesions compatible with cutaneous dermoids (Fig A). A computed tomography scan demonstrated a choroidal osteoma (left eye), hypoplastic left orbit, and a middle cranial fossa mass with low attenuation compatible with a dermoid cyst (Fig B). Chest x-ray revealed scoliosis (Fig C). Magnetic resonance imaging showed a well-defined lesion with irregular margins in the middle cranial fossa and left cerebellopontine angle (Fig D). The protruding mass of the left eye was removed and a diagnosis of Goldenhar syndrome was made. (Magnified version of Fig A-D is available online at www.aaojournal.org).
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