Successful Treatment of Stimulator of Interferon Genes–Associated Vasculopathy of Infantile Onset SAVI Syndrome With Anifrolumab

This case report describes a woman in her 30s who presented with cutaneous lesions since age of 2 to 3 years with erythema and pain on her nose, both cheeks, and ears when exposed to cold temperatures that progressed to nasal and auricular cartilage necrosis and was diagnosed with stimulator of interferon genes–associated vasculopathy with onset in infancy (SAVI syndrome).