血红蛋白
化学
血红素
天冬氨酸
生物化学
氨基酸
酶
作者
Samuel Charache,Bernadine Brimhall,Jones Rt
出处
期刊:PubMed
日期:1975-03-01
卷期号:136 (3): 132-6
被引量:14
摘要
Polycythemia in a black woman was associated with hemoglobin Osler. In this hemoglobin the tyrosine at the penultimate position of the beta chain is replaced by aspartic acid. As a result oxygen affinity of the hemoglobin is very high, heme-heme interaction is absent, and the influence of hydrogen ion and 2,3 diphosphoglycerate on oxygen affinity is attenuated.
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