纤维化
癌症研究
SMAD公司
转化生长因子
信号转导
肺纤维化
医学
生物
病理
细胞生物学
内科学
作者
Tianzhou Zhang,Xiaolin He,Lauren Caldwell,Santosh Kumar Goru,Luisa Ulloa Severino,Monica F. Tolosa,Paraish S. Misra,Caitríona M. McEvoy,Tania Christova,Yong Liu,Cassandra Atin,Johnny Zhang,Catherine Hu,Noah Vukosa,Xiaolan Chen,Adriana Krizova,Anish Kirpalani,Alex Gregorieff,Ruoyu Ni,Kin Chan,Mandeep Gill,Liliana Attisano,Jeffrey L. Wrana,Darren A. Yuen
出处
期刊:Science Translational Medicine
[American Association for the Advancement of Science (AAAS)]
日期:2022-03-23
卷期号:14 (637)
被引量:58
标识
DOI:10.1126/scitranslmed.aaz4028
摘要
Fibrosis is a central pathway that drives progression of multiple chronic diseases, yet few safe and effective clinical antifibrotic therapies exist. In most fibrotic disorders, transforming growth factor-β (TGF-β)-driven scarring is an important pathologic feature and a key contributor to disease progression. Yes-associated protein (YAP) and transcriptional coactivator with PDZ-binding motif (TAZ) are two closely related transcription cofactors that are important for coordinating fibrogenesis after organ injury, but how they are activated in response to tissue injury has, so far, remained unclear. Here, we describe NUAK family kinase 1 (NUAK1) as a TGF-β-inducible profibrotic kinase that is up-regulated in multiple fibrotic organs in mice and humans. Mechanistically, we show that TGF-β induces a rapid increase in NUAK1 in fibroblasts. NUAK1, in turn, can promote profibrotic YAP and TGF-β/SMAD signaling, ultimately leading to organ scarring. Moreover, activated YAP and TAZ can induce further NUAK1 expression, creating a profibrotic positive feedback loop that enables persistent fibrosis. Using mouse models of kidney, lung, and liver fibrosis, we demonstrate that this fibrogenic signaling loop can be interrupted via fibroblast-specific loss of NUAK1 expression, leading to marked attenuation of fibrosis. Pharmacologic NUAK1 inhibition also reduced scarring, either when initiated immediately after injury or when initiated after fibrosis was already established. Together, our data suggest that NUAK1 plays a critical, previously unrecognized role in fibrogenesis and represents an attractive target for strategies that aim to slow fibrotic disease progression.