红细胞痛
医学
发病机制
皮肤病科
流行病学
红斑
疾病
重症监护医学
病理
作者
Elena Gonzalez Caldito,Subuhi Kaul,Natalia Gonzalez Caldito,Warren W. Piette,Shilpa Mehta
标识
DOI:10.1016/j.jaad.2023.02.071
摘要
Erythromelalgia is a rare pain disorder that is underrecognized and difficult-to-treat. It is characterized by episodes of extremity erythema and pain that can be disabling; it may be genetic, related to an underlying systemic disease, or idiopathic. Considering the prominent cutaneous features characteristic of the condition, dermatologists can play an important role in early recognition and limitation of morbidity. The first article in this 2-part continuing medical education series reviews the epidemiology, pathogenesis, clinical manifestations, evaluation, and complications.
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