Launois–Bensaude syndrome involving the orbits

We report the first description of a Launois-Bensaude syndrome involving the orbit.Launois-Bensaude syndrome was diagnosed in a 70-year-old-man who presented with severe bilateral proptosis (Hertel value 26mm). We performed a bilateral transpalpebral orbital decompression by resection of intraorbital fat without bone removal. The surgery was uneventful. The volume of resected orbital fat was 16cc in both sides. Proptosis reduction was 7mm. Postoperative Hertel values were 19mm in both eyes.The proptosis was managed successfully. Orbital lipectomy lead to minimal sequelae and, may be repeated if necessary in this case.