医学
川崎病
血管炎
过敏性紫癜
紫癜(腹足类)
限制
疾病
系统性血管炎
皮肤病科
儿科
免疫学
病理
内科学
机械工程
生态学
动脉
工程类
生物
出处
期刊:Rheumatology
[Oxford University Press]
日期:2020-04-29
卷期号:59 (Supplement_3): iii95-iii100
被引量:22
标识
DOI:10.1093/rheumatology/kez599
摘要
Abstract Vasculitis is a challenging disease for paediatricians. Certain vasculitides are quite common in children whereas others are much rarer compared with adults. The most common vasculitides in childhood are IgA-associated vasculitis (Henoch–Schönlein purpura) and Kawasaki disease, which are usually self-limiting vasculitides although children do develop complications as a result. We now have much better knowledge of how to manage these patients and prevent the deleterious complications. This review provides an up-to-date discussion on childhood vasculitides, including diagnosis, treatment and follow-up strategies, together with a comparison with vasculitides in adults. It also discusses the newly defined monogenic vasculitides that often present during early childhood.
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