Partial anomalous pulmonary venous connection (PAPVC) with intact interatrial septum is an uncommon congenital anomaly, while isolated left pulmonary venous connection with intact interatrial septum is rare. In this report, a 5-year-old girl with chief complains of mild short breath after exercise was diagnosed of anomalous connection between left superior pulmonary vein (LSPV) and left innominate vein by transthoracic echocardiography (TTE) that was confirmed by 3D cardiac CT scanning.