Klippel-Trenaunay and Sturge-Weber Syndromes with Renal Hemangioma and Double Inferior Vena Cava

No AccessJournal of UrologyCase Reports1 Aug 1986Klippel-Trenaunay and Sturge-Weber Syndromes with Renal Hemangioma and Double Inferior Vena Cava Deborah Schofield, Ghazi S. Zaatari, and Brit B. Gay Deborah SchofieldDeborah Schofield , Ghazi S. ZaatariGhazi S. Zaatari , and Brit B. GayBrit B. Gay View All Author Informationhttps://doi.org/10.1016/S0022-5347(17)44899-3AboutPDF ToolsAdd to favoritesDownload CitationsTrack CitationsPermissionsReprints ShareFacebookLinked InTwitterEmail We describe a 3½-year-old boy with the Klippel-Trenaunay and Sturge-Weber syndromes. The child had congenital superficial capillary hemangiomas, congenital glaucoma and mild hydrocephalus. During the first year of life he experienced intermittent hematuria. When he was 3 years old he presented with seizures and left hemihypertrophy first was noted. Several months later radiological examination of a large abdominal mass demonstrated its origin to be in the right kidney. Radical nephrectomy documented the presence of renal hemangioma with complicating perirenal hematoma. A double inferior vena cava was another unexpected surgical finding that complicated the course of this patient. All of these unusual features in these rare syndromes with their clinical, pathogenetic and therapeutic implications are discussed. The differential diagnosis of renal masses in these syndromes also is presented. © 1986 by The American Urological Association Education and Research, Inc.FiguresReferencesRelatedDetailsCited byCampistol J, Agustí C, Torras A, Campo E, Abad C and Revert L (2018) Renal Hemangioma and Renal Artery Aneurysm in the Klippel-Trenaunay SyndromeJournal of Urology, VOL. 140, NO. 1, (134-136), Online publication date: 1-Jul-1988. Volume 136Issue 2August 1986Page: 442-445 Advertisement Copyright & Permissions© 1986 by The American Urological Association Education and Research, Inc.MetricsAuthor Information Deborah Schofield More articles by this author Ghazi S. Zaatari More articles by this author Brit B. Gay More articles by this author Expand All Advertisement PDF downloadLoading ...