医学
暴发性紫癜
皮肤病科
紫癜(腹足类)
生物
生态学
作者
Karol Samman,Cathie-Kim Le,Bruno Michon
出处
期刊:Journal of Pediatric Hematology Oncology
[Ovid Technologies (Wolters Kluwer)]
日期:2022-06-08
卷期号:44 (8): 479-481
被引量:3
标识
DOI:10.1097/mph.0000000000002497
摘要
Idiopathic purpura fulminans (PF) is rare but has been reported in pediatric patients, commonly following infections. We present a case of a 5-year-old boy, heterozygous for factor V Leiden, with no history of recent infections, who presented with PF secondary to acquired protein S deficiency. Despite initial supportive treatment, the patient required surgical fasciotomy and extensive skin grafts. The protein S level normalized 4 months following the presentation. In this context, an autoimmune component with transient anti-protein S antibodies was believed to be involved. This case report highlights the course of idiopathic PF due to noninfectious acquired protein S deficiency.
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