Right ventricular hypertrophy and scarring in mutation positive hypertrophic cardiomyopathy

Hypertrophic cardiomyopathy (HCM) is an autosomal dominant cardiac disorder, characterized by primary left ventricular hypertrophy (LVH), which may result in sudden death secondary to ventricular arrhythmia particularly in the young or diastolic heart failure at any age. Cardiac magnetic resonance imaging (MRI) allows quantification of myocardial thickness, function, left ventricular outflow tract obstruction, and myocardial scarring. Right ventricular hypertrophy and scarring in HCM is not widely documented. A 37-year-old male, with known HCM, presented complaining of intermittent palpitations and occasional light headedness, without exertional symptoms. Electrocardiogram demonstrated LVH by voltage, ( Panel A ) confirmed by echocardiogram …