We report on a case of adrenal angiomyolipoma.The aim was to present a case report and review of the literature about adrenal angiomyolipoma.The case report includes a history of patient data and literature review.The patient was offered adrenalectomy with adrenal gland neoplasms and gave consent. The tumor was completely removed.We present the case of a 55-yr-old patient with a 15 × 16-cm adrenal angiomyolipoma.We performed adrenalectomy with adrenal gland neoplasms.The histopathological features confirmed the diagnosis of adrenal angiomyolipoma. The patient made an uneventful recovery and was normal at the 6-month follow-up.Angiomyolipomas are rare mesenchymal tumors derived from perivascular epithelioid cells. These are commonly found in the kidney. Angiomyolipoma arising in the adrenal is a very rare entity. We present a case of adrenal angiomyolipoma. In our case, the tumor size was (15 × 16 cm), the largest being reported.