Circumferential Pulmonary Ossification From Lung Extraskeletal Osteosarcoma With Mediastinal Shift

Primary extra-skeletal osteosarcoma of the lung is exceedingly rare and associated with a poor prognosis.We present a patient with circumferential pulmonary ossification secondary to lung extra-skeletal osteosarcoma with compressive mediastinal shift who underwent an extra-pleural pneumonectomy that led to resolution of symptoms.This case offers a novel approach to the operative management for primary thoracic osteosarcoma, suggesting that even patients with advanced disease may be surgical candidates, particularly for symptom relief.