医学
硫唑嘌呤
美罗华
霉酚酸酯
皮肤病科
自身免疫
疾病
霉酚酸
自身免疫性疾病
免疫学
耐火材料(行星科学)
粘膜
病理
淋巴瘤
外科
移植
物理
天体生物学
作者
Rosalind Ashton,Hiva Fassihi
出处
期刊:Pediatrics in Review
[American Academy of Pediatrics]
日期:2022-06-01
卷期号:43 (6): 309-321
被引量:1
标识
DOI:10.1542/pir.2021-005125
摘要
Pediatric autoimmune bullous disease is a rare group of blistering skin disorders in children that result from autoimmunity against intercellular and basement membrane antigens in the skin and mucous membranes. Most pediatric cases are treated with oral corticosteroids or longer-term immunosuppressants such as azathioprine or mycophenolate mofetil. Immunomodulating drugs such as rituximab are increasingly being considered as options for refractory disease.
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