半球切除术
医学
颅缝病
半侧巨脑症
神经外科
巨头症
外科
颅缝
骨愈合
发育不良
癫痫
难治性癫痫
先天性疾病
皮质发育不良
病理
精神科
作者
Ogechukwu Ariwodo,Douglas R. Nordli,Nathan J. Ranalli,Alexandra D. Beier
出处
期刊:Journal of neurosurgery
[Journal of Neurosurgery Publishing Group]
日期:2023-11-13
卷期号:6 (20)
摘要
BACKGROUND Hemispherectomy is a surgical procedure reserved for hemispheric intractable epilepsy. Sagittal craniosynostosis is a congenital disorder treated with open or endoscope-assisted approaches for synostosis correction. These procedures are not commonly performed in the same setting. OBSERVATIONS In this report, the authors present a 6-month-old female with sagittal craniosynostosis, hemimegalencephaly, and intractable epilepsy who underwent a left hemispherotomy with open sagittal synostosis correction followed by cranial molding orthosis therapy. LESSONS The report highlights the technical nuances of the procedure, but also discusses the possible genetic disorder responsible for both conditions, megalencephaly-capillary malformation syndrome.
科研通智能强力驱动
Strongly Powered by AbleSci AI