Seronegative basal ganglia encephalitis mimicking dementia of Lewy body

Basal ganglia encephalitis (BGE) is a rare autoimmune disease characterized by movement and neuropsychiatric symptoms and is mostly reported in children and adolescents [ [1] Dale R.C. Merheb V. Pillai S. et al. Antibodies to surface dopamine-2 receptor in autoimmune movement and psychiatric disorders. Brain. 2012; 135: 3453-3468 Crossref PubMed Scopus (278) Google Scholar ] We describe a rare case of seronegative old-onset BGE mimicking dementia of the Lewy body (DLB).