真性红细胞增多症
医学
真性红细胞增多症
红细胞压积
红细胞痛
脑血栓形成
内科学
骨髓增生性肿瘤
胃肠病学
血栓形成
骨髓纤维化
皮肤病科
骨髓
作者
Lei Chen,Han Xiao,Zhiping Hu
标识
DOI:10.1016/j.jstrokecerebrovasdis.2019.04.037
摘要
Polycythemia vera is a chronic myeloproliferative neoplasm, which is primarily characterized by elevated erythrocyte count with the risk of thrombosis, hemorrhage, and vasomotor symptoms. More common reported about bleeding events are gastrointestinal, mucosal, and cutaneous bleeding. Spontaneous cerebral hemorrhage/bleeding is seldom reported. Here, we report the case of a 50-year-old female with polycythemia vera who developed a spontaneous cerebral hemorrhage. She improved significantly after hydroxyurea agent and red cell apheresis, and the hematocrit decreased from 74% to 40%.
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