骨髓增生异常综合症
阿扎胞苷
医学
骨髓
威尼斯人
肿瘤科
白血病
内科学
遗传学
基因
DNA甲基化
生物
基因表达
慢性淋巴细胞白血病
作者
Lisa Pleyer,Mikkael A. Sekeres
标识
DOI:10.1016/s2352-3026(22)00252-6
摘要
Myelodysplastic syndromes, chronic myelomonocytic leukaemia, and acute myeloid leukaemia comprise a spectrum of heterogenous myeloid diseases characterised by abnormal haematopoiesis, a block in differentiation, and haematopoietic insufficiency resulting in cytopenias. These multiclonal processes show considerable biologic, phenotypic, genetic, and clinical overlap. In recognition of this continuum, WHO has recently renamed the former category of myelodysplastic syndromes with excess blasts-2 (defined as having ≥10% and <20% bone marrow blasts) to “myelodysplastic syndromes/acute myeloid leukaemia”.
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